A young child is seen with hypertension. He also is found to have large hemangiomas on his face, eyes, and trunk. Work up reveals a pheochromocytoma. What is the greatest risk to the patient?
Select Your Answer:
Von Hippel-Lindau (VHL) disease causes adenomas of the viscera, especially renal cell carcinoma.
It is a rare genetic disease that is inherited in an autosomal dominant pattern.
There is a defect in VHL tumor suppressor gene.
About half of patients with VHL disease have retinal hemangioblastomas.
Adult Lab Normals
Pediatric Lab Normals
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